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Drugs in development · updated 30 October 2026

Neuroendocrine tumor: drugs in development

Rare diseasePrevalence 1-5 / 10 000 according to Orphanet · ORPHA:877

As of 30 October 2026 there are 89 active clinical trials (recruiting or ongoing, phases I–III) on 84 drugs for neuroendocrine tumor. 43 are experimental, that is not yet approved in the United States.

89Active trials
43Experimental drugs
4Experimental, in phase III

Summary updated every week · data as of 30 October 2026. In Phuturdex you get the full detail of every drug and an email when an alert is published on the ones you follow.

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Experimental drugs

Not yet approved by the US FDA for any indication.

DrugMost advanced phaseActive trialsReference trial
177Lu-DOTATOCLutetium Lu 177-EdotreotideIII3NCT05387603
ZanzalintinibXL092II–III3NCT06943755
ErsodetugRZ358III1NCT06881992
RYZ101III1NCT05477576
Lu-177-DOTATATEI–II2NCT04086485
SurufatinibSulfatinib, Sevsury®I–II2NCT06038461
TriapineII2NCT05724108
177Lu-OctreotateII1NCT02754297
23ME-00610I–II1NCT05199272
68Ga-HA-DOTATATEII1NCT04888481
AdebrelimabSHR-1316, AdebelimabII1NCT06764368
AlphaMedixII1NCT05153772
ApatinibRivoceranibII1NCT06764368
CRN09682I–II1NCT07129252
CTX-471II1NCT07684170
CVM-1118II1NCT03600233
Ga-68-DOTATATEII1NCT03206060
GocatamigI–II1NCT04471727
GuaranaII1NCT07151391
IBI310II1NCT05165407
Ifinatamab DeruxtecanI–II1NCT04471727
Lu-177-DOTA-OctreotideII1NCT04917484
MT-4561I–II1NCT06943521
PM8002II1NCT05879055
SintilimabSinitilimab, SindilimabII1NCT05165407
Terbium 161II1NCT07404176
TirapazamineI–II1NCT02174549
177Lu-PP-F11NI1NCT02088645
[68Ga]Ga-FAPI-46Gallium Ga 68 FAPi-46I1NCT04459273
ADCT-701I1NCT06041516
BL-M14D1I1NCT06505824
CID-078I1NCT06577987
IM-1340I1NCT07890246
Lu-177I1NCT05249114
NN3201I1NCT06805825
PeposertibI1NCT04750954
PorustobartHBM4003I1NCT05167071
RYZ401I1NCT07165132
Sapu003I1NCT07369505
131I-MIBGEarly I1NCT03044977

Sorted by most advanced phase and number of active trials. Showing 40 of 43 drugs.

Approved drugs in new trials

Approved by the US FDA for at least one indication, not necessarily this disease, and now in active trials on it.

DrugMost advanced phaseActive trialsReference trial
LutatheraLutetium Lu 177 Dotatate, 177Lu-DOTATATEIII10NCT06878664
EverolimusRAD001, EveroliumusII–III7NCT06943755
TemozolomideTemodal, TemodarIII5NCT07185672
CapecitabineXeloda, Capectitabine TabletsIII3NCT07185672
LanreotideSomatuline Depot®III3NCT05477576
Cabozantinib S-malateCabometyx®, Cometriq®III2NCT03375320
OctreotideSandostatin LAR@, Bynfezia Pen®III2NCT00569127
18F-DOPA18F-FDOPA, Fluorodopa F 18III1NCT04706910
Bevacizumabavastin, MVASIIII1NCT00569127
Fluorouracil5-Fluorouracil, AdrucilIII1NCT04919226
FurosemideLasix Onyu®, Furoscix®III1NCT04706910
OxaliplatinOxaliplatine, OxaliplainIII1NCT04919226
PaltusotinePalsonify®III1NCT07087054
SunitinibSutent®, Sunitinib Accord®III1NCT05477576
Telotristat EthylXermelo®III1NCT04810091

Sorted by most advanced phase and number of active trials. Showing 15 of 41 drugs.

All 84 drugs, with the details

In Phuturdex every drug has all its trials, sponsors and countries, FDA and EMA approvals, orphan designations and safety alerts. Free until 31 March 2027.

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Specific forms

Broader categories

Source: Phuturdex analysis of ClinicalTrials.gov data (U.S. National Library of Medicine), updated 30 October 2026. Active trials = recruiting or ongoing, phases I–III, with at least one identified drug; phase and sites refer to the trials on this disease. Disease name: Wikidata; NLM MeSH term: D018358 “Neuroendocrine Tumors”. Prevalence: Orphanet.

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